Dejerine-Sottas syndrome (DSS) is a rare, inherited neurological disorder that progressively impairs movement. It's also known as hereditary motor and sensory neuropathy type III (HMSN III).
Understanding DSS
DSS affects the peripheral nerves—the nerves located outside the brain and spinal cord. These nerves become enlarged or thickened, causing muscle weakness. The condition gradually worsens over time.
- Key features of DSS:
- Inherited condition: Passed down through families.
- Peripheral nerve damage: Leading to muscle weakness.
- Progressive nature: Symptoms worsen over time.
- Muscle weakness and atrophy: Loss of muscle mass and function.
- Sensory loss: Reduced feeling in the limbs.
The provided links refer to various state Department of Health and Human Services (DHHS) agencies. These are governmental bodies responsible for public health and related services. They are not directly related to the definition of Dejerine-Sottas syndrome itself.
