It appears you're asking about Dejerine-Sottas syndrome, not Degeneres syndrome. Dejerine-Sottas syndrome (DSS) is a rare, inherited neurological disorder that progressively impacts movement capabilities.
Understanding Dejerine-Sottas Syndrome (DSS)
DSS is characterized by the enlargement or thickening of peripheral nerves, which are the nerves outside the brain and spinal cord. This thickening disrupts nerve function leading to:
- Muscle Weakness: The most notable symptom is a gradual weakening of muscles due to compromised nerve signaling.
- Progressive Nature: The condition is progressive meaning symptoms worsen over time.
Key Features of DSS
| Feature | Description |
|---|---|
| Type | Inherited neurological condition |
| Affected Area | Peripheral nerves (nerves outside the brain and spinal cord) |
| Primary Symptom | Gradual muscle weakness |
| Nerve Changes | Enlargement or thickening of peripheral nerves |
| Progression | Symptoms worsen over time |
| Inheritance | Inherited genetic condition |
Inherited Aspects of DSS
As noted in the provided information, Dejerine-Sottas syndrome is an inherited condition. This means it is passed down through families.
Summary
In summary, Dejerine-Sottas syndrome is an inherited neurological disorder affecting the peripheral nerves. These nerves thicken, causing progressive muscle weakness.
