UIP, or Usual Interstitial Pneumonia, is also known as idiopathic pulmonary fibrosis, Hamman–Rich syndrome, and idiopathic fibrosing alveolitis.
Here's a breakdown of these terms:
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Idiopathic Pulmonary Fibrosis (IPF): This is the most common and widely recognized synonym for UIP. The term "idiopathic" means the cause is unknown, and "pulmonary fibrosis" refers to the scarring of the lung tissue.
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Hamman–Rich Syndrome: This is an older term for a rapidly progressive form of UIP.
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Idiopathic Fibrosing Alveolitis: This term emphasizes the inflammation and subsequent fibrosis (scarring) within the alveoli (air sacs) of the lungs. Like IPF, the cause is unknown.
In essence, all these terms can refer to the same underlying lung disease characterized by scarring and inflammation, leading to difficulty breathing and reduced oxygen levels. According to the provided reference, UIP is a pulmonary disease of unknown etiology characterized clinically by severe hypoxemia and cyanosis.
| Term | Description |
|---|---|
| Idiopathic Pulmonary Fibrosis | Most common term; emphasizes unknown cause and lung scarring. |
| Hamman–Rich Syndrome | An older term, usually referring to a rapidly progressing form. |
| Idiopathic Fibrosing Alveolitis | Highlights inflammation and fibrosis in the alveoli, with an unknown cause. |
